Hemifacial hypertrophy abbreviated as (HFH) is rare congenital disease characterized by unilateral enlargement of the head and teeth. It is classified as true. Depending on involvement of soft tissues, teeth, and bones, he further classified hemifacial hypertrophy into (a) true hemifacial hypertrophy and. Two cases of congenital hemifacial hypertrophy are described. To our knowledge , this is the first report of this syndrome in a black African population. Possible.

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Eruption pattern on right side is far advanced than the left side with broad and thick alveolar process.

The patient was of normal built and intelligence. Log in Sign up. The affected side tissue growth occurs in an exponential manner in comparison to the uninvolved side resulting in facial asymmetry following a skeletal arrest. Limited cases of hemifacial hyperplasia have been documented.

Br J Oral Maxillofac Surg. Open in a separate window. Wider and thicker mandibular alveolar process on right side, particularly in the premolar-molar region. Based on clinicoradiological findings, the diagnosis of THFH was established. Unilateral enlargement of right side of the face. Medical examination did not reveal any other health issues. Plastic and Reconstructive Surgery.

Hemifacial hypertrophy | Radiology Reference Article |

We report an interesting case of true hemifacial hyperplasia THFH in a year-old male, discussing clinical features, imaging findings, and differential diagnosis in detail to supplement the current literature. Diffuse enlargement of the right side of face beginning abruptly at the midline and deviation of nose, mouth and chin toward the left side.


Subtle, asymmetric variation of the contralateral structures of the head and face occur commonly in the general population in the absence of any local lesion or condition.

Our patient had the classical clinical features of THFH such as unilateral overgrowth of the orofacial soft tissues, tongue, teeth, and bones causing an obvious asymmetry of the right side of the face.

Congenital Hemifacial Hyperplasia CHH is a rare developmental malformation exhibited by a unilateral enlargement of hard and soft tissues of the face.

The prevalence rate of HFH is 1: Congenital hemifacial hyperplasia is a rare developmental disorder of unknown etiology, characterized by a marked unilateral facial asymmetry.

Family history was noncontributory. Orofacial soft tissues — Soft tissues around the mouth.

Congenital Hemifacial Hyperplasia: Clinical Presentation and Literature Review

The patient had visited multiple plastic surgery units since childhood and had been diagnosed with hemihypertrophy [ Figure 1 ]. In addition, all these conditions have distinct features that differ from those of HFH radiographically and clinically.

The surface of the gingival tissue and palate on the right side was granular in appearance. Similarly, right permanent mandibular lateral incisor, canine, first premolar, and second premolar were larger cervicoincisally, mesiodistally, and labiolingually than those of the left side Table 2.

Hemifacial hypertrophy: Exploring new avenues of treatment modalities

The right buccal mucosa was thickened and hung in pendulous folds Figure 4. This article presents a unique case report of a typical case of CHH with hypertrophhy detailed emphasis on diagnostic criteria clinical and radiographic appearance thus emphasizing to all the readers its importance.

Abstract Congenital hemifacial hyperplasia CHH is a rare congenital malformation characterized by marked unilateral overdevelopment of hard and soft tissues of the face. In cases with hemifacial myohyperplasia, there is an enlargement of the muscle mass of the facial muscles with ipsilateral hypoplasia of the facial skeleton [ 20 ].


Ipsilateral pinna and pupil may be enlarged, but an increase in size of the inner ear or globe of the eye has not been reported [ 4 ]. Clinical and imaging findings of true hemifacial hyperplasia.

Hemifacial hyperplasia HFH is a rare developmental anomaly exhibiting asymmetric facial growth by unilateral localized enlargement of all tissues in the affected area that is facial hemifacia, teeth, and soft tissues [ 5 ]. Involvement of orofacial structures is related to asymmetric morphogenesis of teeth, hypertropyh, and soft tissues. Of note, our case hemidacial with marked dental abnormalities like precocious tooth development and macrodontia.

In addition, this technique is more time consuming, as the surgeon has to move the laser cannula relatively slowly through then skin to allow for necessary time for the laser-tissue interaction and a second pass with a suction cannula is necessary for fat aspiration.

About Blog Go ad-free. Condylectomy is seldom hemidacial but had been reported by Trapp. Author information Copyright and License information Disclaimer.

Looking For More Hypertrpphy Intraoral photograph showing velvety buccal mucosa hanging in pendulous folds and granular gingival surface along with macrodontic permanent right lateral incisor and canine.